Degos Disease which is also called malignant atrophic papulosis is a disease named after Robert degos who recognised it as a clinical entity in 1942. It is a very rare vasculopathy results to blockage of vessels and tissue infarction after effecting the inner linning of veins and arteries.
Some ailments like bowel ischemia (mesenteric ischemia or ischemic colitis), chronic skin lesions, ocular lesions, strokes, spinal lesions, mononeuritis multiplex, epilepsy, headaches or cognitive disorders can occur as a result of blood vessels that has been affected;those that can be affected include those supplying the skin,gastrointestinal tract, and central nervous system.
The outcome of this disease can be fatal with a median survival of 2 to 3 years,[1] although some appear to have a benign form (Degos acanthoma) which affects only the skin. There are fewer than fifty living patients at present known worldwide, and less than 200 reported in the medical literature. Treatment options are imited, consist mainly of Antiplatelet drugs or anticoagulants or immunosuppressants, and effect of treatment is limited to case reports.
It has been suggested that this is not a separate disorder, but the final result of several vascular systemic disorders.
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